A Rare Variant of Hypogenetic Lung Syndrome mimicking Scimitar Vein

Hypogenetic lung syndrome (HLS), also known as scimitar syndrome, is a rare and well-known congenital condition which includes hypoplastic right pulmonary artery and lung, right displacement of the heart, anomalous systemic arterial supply to lung and a characteristically curved anomalous right pulmonary vein draining into inferior vena cava. In exceptional cases, the anomalous pulmonary vein may drain into left atrium. We here report a case of a 17-year-old girl with a rare variant of HLS diagnosed by means of multimodality imaging and treated with percutaneous occlusion of the aortopulmonary collateral.