Children with neuromuscular disorders (NMDs) are at high risk for respiratory complications due to impaired cough and weakness of respiratory muscles. Effective cough is essential for airway clearance, infections’ prevention, and maintaining lung function. This narrative review explores the physiology of cough, the consequences of cough insufficiency, and methods for assessing respiratory function in pediatric NMDs. It discusses current care strategies including airway clearance techniques, respiratory muscle training, and preventive and supportive interventions. Emphasis is placed on multidisciplinary management and early intervention to improve outcomes and quality of life.

Managing Cough in Pediatric Neuromuscular Disorders: Lung Function and Care Strategies

Foti Randazzese, Simone;Manti, Sara
Ultimo
2025-01-01

Abstract

Children with neuromuscular disorders (NMDs) are at high risk for respiratory complications due to impaired cough and weakness of respiratory muscles. Effective cough is essential for airway clearance, infections’ prevention, and maintaining lung function. This narrative review explores the physiology of cough, the consequences of cough insufficiency, and methods for assessing respiratory function in pediatric NMDs. It discusses current care strategies including airway clearance techniques, respiratory muscle training, and preventive and supportive interventions. Emphasis is placed on multidisciplinary management and early intervention to improve outcomes and quality of life.
2025
Inglese
Inglese
STAMPA
Si
Si, OA ibrido
Multidisciplinary Digital Publishing Institute (MDPI)
12
10
1
17
17
https://pubmed.ncbi.nlm.nih.gov/41153559/
Internazionale
Esperti anonimi
care strategies; cough; lung function; neuromuscular disorders; pediatrics
no
info:eu-repo/semantics/article
Foti Randazzese, Simone; Fenu, Grazia; Calogero, Claudia; Lombardi, Enrico; Manti, Sara
14.a Contributo in Rivista::14.a.1 Articolo su rivista
5
262
none
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Utilizza questo identificativo per citare o creare un link a questo documento: https://hdl.handle.net/11570/3342551
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